SICKLE CELL DISEASE

Sickle cell disease is a hereditary blood disorder caused by abnormal haemoglobin found in red blood cells. 

SUPPORTING STUDENTS             MORE INFORMATION

Causes of sickle cell disease

• In people with sickle cell disease, the shape and texture of the blood cells can change.
• The cells become hard and sticky and are shaped like sickles, or crescents.
• The cells die prematurely leading to a shortage of red blood cells.
• This causes the symptoms of anaemia such as tiredness and breathlessness.

Symptoms of sickle cell disease

• If you have sickle-cell disease, your blood cells can get stuck when moving through small blood vessels, stopping the supply of oxygen to parts of your body.
• This is known as a 'sickle crisis'.
• This can cause pain, tissue damage, and can lead to other serious complications, such as a stroke, or blindness.

Treatment for sickle cell disease

• The only cure for sickle cell disease is a stem cell transplant.
• The symptoms of sickle cell disease can be treated and people with the condition can learn how to help prevent a sickle crisis from happening.

Common triggers of a sickle cell crisis

• Infections
• Dehydration
• Stress
• Excessive temperatures
• Excessive physical activity

Supporting students with sickle cell disease

• Meet parents/carers and where available the Sickle Cell Clinical Nurse Specialist to draw up an Individual Healthcare Plan. This will include what to do in the case of a sickle cell crisis. 
• Ensure all staff are aware of adjustments agreed to support the student make the most of school.

Fluid intake and temperature

• Allow students to have a water bottle available always. 
• Allow students to use the toilet as required without fuss. 
• During cold weather plan for the student to access an indoor space with some friends so they do not feel isolated.

Physical needs

• Meet with parents/carers and the student to plan support around their physical needs.
• Use of the school lift may be required
• Allow the student to set their own pace during PE lessons.
• If an outdoor PE session takes place on a cold day provide an alternative indoor PE activity.
• Following swimming allow time to get properly dry and to dress warmly. 

School absence

• If a student is absent for more than 2 days email or post-school work home. Falling behind can cause additional stress. 
• Allow time to catch up with missed work.
• Check in with a student on their return and help plan a catch-up schedule. 
• If admitted to hospital contact the hospital school staff promptly with details of work.

School trips

• Consideration needs to be given to allow more frequent toilet stops on longer journeys.
• Find the location of the nearest Hospital Accident & Emergency department.
• Get information and permission for the administration of medication in case of a crisis.

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